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KMID : 0352119920080020184
Journal of Kyung Hee University
1992 Volume.8 No. 2 p.184 ~ p.188
Tuberous Sclerosis in Sibling




Abstract
Tuberous Sclerosis is a complex neurocutaneous disorder, inherited as an autosomal dominant trait, in which adenoma sebaceum, mental retardation, seizures, renal tumor and phakoma of retina are particulary frequent, in which renal tumors are
usually
angiomyolipoma. We report cases of tuberous sclerosis in sibling associated with bilateral renal angiomyolipomas treated with selective renal arterial embolization.
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