KMID : 0352119920080020184
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Journal of Kyung Hee University 1992 Volume.8 No. 2 p.184 ~ p.188
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Tuberous Sclerosis in Sibling
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Abstract
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Tuberous Sclerosis is a complex neurocutaneous disorder, inherited as an autosomal dominant trait, in which adenoma sebaceum, mental retardation, seizures, renal tumor and phakoma of retina are particulary frequent, in which renal tumors are
usually
angiomyolipoma. We report cases of tuberous sclerosis in sibling associated with bilateral renal angiomyolipomas treated with selective renal arterial embolization.
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KEYWORD
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